A rare case of childhood interstitial lung disease attributed to desquamative interstitial pneumonia

Samiksha Kamble¹, Ketaki Utpat², Gayathri Amonkar³, Unnati Desai²

Keywords: Child interstitial lung disease, Desquamative interstitial pneumonia, Transbronchial lung biopsy

DOI: 10.32677/yjm.v2i2.4098

DOI URL: https://doi.org/10.32677/yjm.v2i2.4098

Publish Date: 28-09-2023

Pages: 112 - 114

Views: 2

Downloads: 3

Author Affiliation:

¹Senior Registrar, 
²Associate Professor, Department of Pulmonary Medicine,
³Associate Professor, Department of Pathology, T. N. Medical College, B. Y. L. Nair Hospital, Mumbai, Maharashtra, India

Abstract

Desquamative interstitial pneumonia is a rare form of interstitial lung disease in children that can be idiopathic but is usually associated with an inborn error of surfactant metabolism. We reported DIP in a thirteen-year-old girl who was referred to our outpatient clinic because of worsening dyspnoea. High-resolution computed tomography showed ground-glass attenuation with honeycombing and intralobular, interstitial septal thickening suggestive of an interstitial lung disease. Transbronchial lung biopsy was performed and histopathology findings were consistent with desquamative interstitial pneumonia. The patient was started on steroid therapy with oxygen support. Unfortunately, she died a month after being diagnosed due to disease progression.